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Search Results to Pamela Zeitlin

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One or more keywords matched the following items that are connected to Zeitlin, Pamela

Item TypeName
Academic Article Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis.
Academic Article Inflammatory and microbiologic markers in induced sputum after intravenous antibiotics in cystic fibrosis.
Academic Article Safety and tolerability of denufosol tetrasodium inhalation solution, a novel P2Y2 receptor agonist: results of a phase 1/phase 2 multicenter study in mild to moderate cystic fibrosis.
Academic Article Patients with mutations in Gsalpha have reduced activation of a downstream target in epithelial tissues due to haploinsufficiency.
Academic Article Randomized, double-blind, placebo-controlled, dose-escalating study of aerosolized interferon gamma-1b in patients with mild to moderate cystic fibrosis lung disease.
Academic Article Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis.
Academic Article Repeated aerosolized AAV-CFTR for treatment of cystic fibrosis: a randomized placebo-controlled phase 2B trial.
Concept Cystic Fibrosis
Concept Cystic Fibrosis Transmembrane Conductance Regulator
Academic Article Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial.
Academic Article Pharmacokinetics and safety of cavosonstat (N91115) in healthy and cystic fibrosis adults homozygous for F508DEL-CFTR.
Academic Article Phase I trial of intranasal and endobronchial administration of a recombinant adeno-associated virus serotype 2 (rAAV2)-CFTR vector in adult cystic fibrosis patients: a two-part clinical study.
Academic Article Direct interactions between ENaC gamma subunit and ClCN2 in cystic fibrosis epithelial cells.
Academic Article Evaluation of exposure and health care worker response to nebulized administration of tgAAVCF to patients with cystic fibrosis.
Academic Article Current treatment recommendations for correcting vitamin D deficiency in pediatric patients with cystic fibrosis are inadequate.
Academic Article A multicenter study of the effect of solution temperature on nasal potential difference measurements.
Academic Article Pharmacoproteomics of 4-phenylbutyrate-treated IB3-1 cystic fibrosis bronchial epithelial cells.
Academic Article Pseudomonas aeruginosa: can studies in engineered cells tell us why is it such a problem in people with cystic fibrosis? Focus on "Cystic fibrosis transmembrane conductance regulator and caveolin-1 regulate epithelial cell internalization of Pseudomonas aeruginosa".
Academic Article Respiratory epithelial gene expression in patients with mild and severe cystic fibrosis lung disease.
Academic Article Selective inhibition of endoplasmic reticulum-associated degradation rescues DeltaF508-cystic fibrosis transmembrane regulator and suppresses interleukin-8 levels: therapeutic implications.
Academic Article Emerging drug treatments for cystic fibrosis.
Academic Article Interference with ubiquitination in CFTR modifies stability of core glycosylated and cell surface pools.
Academic Article Applications of proteomic technologies for understanding the premature proteolysis of CFTR.
Academic Article Digitoxin for Airway Inflammation in Cystic Fibrosis: Preliminary Assessment of Safety, Pharmacokinetics, and Dose Finding.
Academic Article N-acetylcysteine enhances cystic fibrosis sputum penetration and airway gene transfer by highly compacted DNA nanoparticles.
Academic Article Biodegradable polymer nanoparticles that rapidly penetrate the human mucus barrier.
Academic Article Emerging drug treatments for cystic fibrosis.
Academic Article Dual activation of CFTR and CLCN2 by lubiprostone in murine nasal epithelia.
Academic Article Gene expression profile analysis of 4-phenylbutyrate treatment of IB3-1 bronchial epithelial cell line demonstrates a major influence on heat-shock proteins.
Academic Article Is it go or NO go for S-nitrosylation modification-based therapies of cystic fibrosis transmembrane regulator trafficking?
Academic Article Lubiprostone activates non-CFTR-dependent respiratory epithelial chloride secretion in cystic fibrosis mice.
Academic Article De novo biosynthetic profiling of high abundance proteins in cystic fibrosis lung epithelial cells.
Academic Article Spiperone, identified through compound screening, activates calcium-dependent chloride secretion in the airway.
Academic Article Atypical cystic fibrosis and CFTR-related diseases.
Academic Article Cystic fibrosis presenting as recurrent pancreatitis in a young child with a normal sweat test and pancreas divisum: a case report.
Academic Article CHOP transcription factor mediates IL-8 signaling in cystic fibrosis bronchial epithelial cells.
Academic Article A phase I trial of intranasal Moli1901 for cystic fibrosis.
Academic Article Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate.
Academic Article Variant cystic fibrosis phenotypes in the absence of CFTR mutations.
Academic Article Transient effectiveness of vitamin D2 therapy in pediatric cystic fibrosis patients.
Academic Article CFTR is a negative regulator of NFkappaB mediated innate immune response.
Academic Article Clinical Phenotypes and Genotypic Spectrum of Cystic Fibrosis in Chinese Children.
Academic Article Modulation of deltaF508 cystic fibrosis transmembrane regulator trafficking and function with 4-phenylbutyrate and flavonoids.
Academic Article Cystic fibrosis and estrogens: a perfect storm.
Academic Article cis-Acting elements within CFTR 5'-flanking DNA are not sufficient to decrease gene expression in response to phorbol ester.
Academic Article Repeated adeno-associated virus serotype 2 aerosol-mediated cystic fibrosis transmembrane regulator gene transfer to the lungs of patients with cystic fibrosis: a multicenter, double-blind, placebo-controlled trial.
Academic Article Correlation between DNA transfer and cystic fibrosis airway epithelial cell correction after recombinant adeno-associated virus serotype 2 gene therapy.
Academic Article The penetration of fresh undiluted sputum expectorated by cystic fibrosis patients by non-adhesive polymer nanoparticles.
Academic Article Ubiquitin C-terminal hydrolase-L1 protects cystic fibrosis transmembrane conductance regulator from early stages of proteasomal degradation.
Academic Article Variants in mannose-binding lectin and tumour necrosis factor alpha affect survival in cystic fibrosis.
Academic Article Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials.
Academic Article Chemical rescue of deltaF508-CFTR mimics genetic repair in cystic fibrosis bronchial epithelial cells.
Academic Article Positive expiratory pressure changes aerosol distribution in patients with cystic fibrosis.
Academic Article Antibody microarrays: analysis of cystic fibrosis.
Academic Article Dietary supplement use in pediatric patients with cystic fibrosis.
Academic Article Cystic fibrosis transmembrane regulator protein mutations: 'class' opportunity for novel drug innovation.
Academic Article Levofloxacin pharmacokinetics in adult cystic fibrosis.
Academic Article Can curcumin cure cystic fibrosis?
Academic Article Description of a standardized nutrition classification plan and its relation to nutritional outcomes in children with cystic fibrosis.
Academic Article Serum proteomic signature for cystic fibrosis using an antibody microarray platform.
Academic Article No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
Academic Article Acidic pH hyperpolarizes nasal potential difference.
Academic Article Cystic fibrosis and sinusitis in children: outcomes and socioeconomic status.
Academic Article Airway microbiota across age and disease spectrum in cystic fibrosis.
Academic Article Effect of ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis patients with G551D-CFTR.
Academic Article Cystic fibrosis transmembrane conductance regulator function, not TAS2R38 gene haplotypes, predict sinus surgery in children and young adults with cystic fibrosis.
Academic Article Changes in mucociliary clearance over time in children with cystic fibrosis.
Academic Article Effect of apical chloride concentration on the measurement of responses to CFTR modulation in airway epithelia cultured from nasal brushings.
Academic Article Downregulation of epithelial sodium channel (ENaC) activity in human airway epithelia after low temperature incubation.
Academic Article Characterizing mucociliary clearance in young children with cystic fibrosis.
Academic Article Expanding CFTR Modulator Testing to Carriers of CFTR Variants.
Academic Article Elexacaftor is a CFTR potentiator and acts synergistically with ivacaftor during acute and chronic treatment.
Academic Article Measurements of spontaneous CFTR-mediated ion transport without acute channel activation in airway epithelial cultures after modulator exposure.
Academic Article Receptor-mediated activation of CFTR via prostaglandin signaling pathways in the airway.
Academic Article The Changing Face of Cystic Fibrosis: An Update for Anesthesiologists.
Academic Article Net benefit of ivacaftor during prolonged tezacaftor/elexacaftor exposure in vitro.
Academic Article IL-13-programmed airway tuft cells produce PGE2, which promotes CFTR-dependent mucociliary function.

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